formula contains some bound galactose (eg Isomil 1.4
mgI100 ml). The availability of this bound galactose is
under question (see below). Once solid foods are started
there are further issues concerning galactose sources. Table
1 gives estimates of potential intake.
Once solid foods are commenced the Handbook for
Galactosemia (Working Group for Australasia Society of
Inborn Errors of Metabolism, 1998) recommends that
the following foods be avoided:
Milk and milk products, except for mature cheese
in which the galactose has been broken down
during the production process. These foods are
major sources of lactose, which consists of a unit
of glucose and a unit of galactose. It is important
for patients and their families to understand that
low lactose or lactose reduced products may still
contain their full quota of galactose. During the
maturing process of cheese, however, the majority
of galactose is broken down. In view of the
usefulness of cheese as a contributor of calcium in
the diet, cheeses with less than 0.1% galactose
(100 mg per 100 g cheese) may be included.
Lactose, used as an ingredient and canier for flavour
in foods, as well as in some medications. Lactose
is used as a camer of flavourings and salt in foods.
In Australia, The Smith's Snackfood Company
has provided data to show that the flavour can
contain between 8.8% and 42% lactose. This can
result in a product with up to 11.3% lactose (2.8
g lactose per 25 g packet of extruded cheese snacks,
0.55 g lactose per 25 g packet flavoured potato
chips). Families also need to check the use of
lactose as a flavour carrier in take-away foods.
Chickpeas (garbanzo beans), beans or gram flour,
homrnos, dahl and felafel made on chickpeas.
Fermented soy products eg miso, tempeh, some
soy sauce where bound galactose may be
released.
formula contains some bound galactose (eg Isomil 1.4
mgI100 ml). The availability of this bound galactose is
under question (see below). Once solid foods are started
there are further issues concerning galactose sources. Table
1 gives estimates of potential intake.
Once solid foods are commenced the Handbook for
Galactosemia (Working Group for Australasia Society of
Inborn Errors of Metabolism, 1998) recommends that
the following foods be avoided:
Milk and milk products, except for mature cheese
in which the galactose has been broken down
during the production process. These foods are
major sources of lactose, which consists of a unit
of glucose and a unit of galactose. It is important
for patients and their families to understand that
low lactose or lactose reduced products may still
contain their full quota of galactose. During the
maturing process of cheese, however, the majority
of galactose is broken down. In view of the
usefulness of cheese as a contributor of calcium in
the diet, cheeses with less than 0.1% galactose
(100 mg per 100 g cheese) may be included.
Lactose, used as an ingredient and canier for flavour
in foods, as well as in some medications. Lactose
is used as a camer of flavourings and salt in foods.
In Australia, The Smith's Snackfood Company
has provided data to show that the flavour can
contain between 8.8% and 42% lactose. This can
result in a product with up to 11.3% lactose (2.8
g lactose per 25 g packet of extruded cheese snacks,
0.55 g lactose per 25 g packet flavoured potato
chips). Families also need to check the use of
lactose as a flavour carrier in take-away foods.
Chickpeas (garbanzo beans), beans or gram flour,
homrnos, dahl and felafel made on chickpeas.
Fermented soy products eg miso, tempeh, some
soy sauce where bound galactose may be
released.
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