Table 1
Patients’ characteristics.
Controls Non-PAH
mPAP < 25 mmHg
PAH
mPAP ≥ 25 mmHg
(n = 37) (n = 37) (n = 15)
Age 59.0 ± 5.8 56.0 ± 12.6 58 ± 14.8
Female 32 (86%) 31 (84%) 12 (80%)
Height (cm) 158.3 ± 7.0 154.9 ± 6.9 158.1 ± 9.5
Body weight (kg) 49.0 ± 8.4 48.6 ± 8.2 52.3 ± 9.3
Body mass index 21.0 ± 1.4 20.2 ± 2.8 20.8 ± 2.8
6MWD (m) – 411.4 ± 93.8 374.2 ± 58.9†
SSc – 26 (70%) 10 (67%)
CTD except SSc – 11 (30%) 5 (33%)
Log BNP – 2.03 ± 0.24 2.10 ± 0.26
%DLco (%) – 53.5 ± 16.1 39.6 ± 13.6
mPAP (mmHg) – 17.0 ± 4.1 32.1 ± 7.4†
PAWP (mmHg) – 8.2 ± 4.1 10.5 ± 2.3†
PVR (dynes s m2 cm5) – 112.2 ± 52.9 286.9 ± 101.6†
CO (L/min) – 6.0 ± 1.3 6.7 ± 2.2
Rest SBP/DBP (mmHg) 120.3 ± 25.5/69.0 ± 11.7 113.7 ± 24.2/64. 1 ± 9.8 118.6 ± 14.2/66.6 ± 11.1
Rest heart rate (bpm) 72.2 ± 13.1 74.6 ± 11.6 79.7 ± 16.4
Post SBP/DBP (mmHg) 137.3 ± 25.0/81.6 ± 21.3 145.2 ± 24.8* /75.9 ± 13.2 148. 7 ± 24.6** /82.0 ± 13.4
Post heart rate (bpm) 86.1 ± 14.8 104.1 ± 22.2* 118. 7 ± 10.2**
PAH, pulmonary arterial hypertension; 6MWD, 6-min-walk distance; SSc, systemic sclerosis; CTD, connective tissue disease; BNP, brain natriuretic peptide; %DLco, carbon
monoxide diffusion capacity by body surface; mPAP, mean pulmonary arterial pressure; PAWP, pulmonary arterial wedge pressure; PVR, pulmonary vascular resistance; CO,
cardiac output; SBP, systolic blood pressure; DBP, diastolic blood pressure.
* p < 0.05, controls vs. non-PAH. ** p < 0.05, controls vs. PAH. † p < 0.05, non-PAH vs. PAH