KD accounted for more than half of the cases in this group (60%), with all of the patients being younger than 6 years old. Fourteen of them had received aspirin and intravenous Ig treatment. Those children with HLH and histiocytosis had relatively unfavorable outcomes compared to the other etiologies. Two of the three patients with HLH and one of the two patients with histiocytosis died despite intensive chemotherapy or bone marrow transplant. The patient with myelodysplastic syndrome also died after steroid pulse therapy and bone marrow transplant.