Hearing loss pattern depends on the localization of the demyelinization plaque. If demyelinization occurs on the root of cochlear nerve, high frequency hearing loss is observed like in cochlear nerve masses. Low frequency hearing loss is detected in cases with demyelinization in auditory brain stem. Edema around the demyelinization area may mimic the cochlear type Sudden sensorineural hearing loss [2]. In our case rapid hearing improvement may be seen due to regression of demyelinization area and absorption of the edema in auditory tract.