Sudden sensorineural hearing loss owing to Multiple sclerosis is seen due to demyelinization at cranial nerve or auditory brainstem. In most cases in the literature demyelinization plaque is detected at root of the cochlear nerve, besides lesions through the nerve were also reported [4, 7, 9]. In the present case a large demyelinization plaque was detected on the proximal part of the right cochlear nerve and cochlear nucleus which disappeared on the 5th day of the medical therapy and hearing gain was also observed.