Abstract
Accessory auricle is a congenital anomaly of a pinna which is commonly localized anterior to the
tragus. It contains a small piece of cartilage underneath. The prevalence of accessory auricle is 0.2-
0.47%. It can be found isolated or related with otherassociated disorders. Excision is usually indicated
for cosmetic reason. Here, we present a case of isolated accessory auricle and review of the
literature, including the embryological development of pinna and a genetic - linkage analysis.