La Maladie Bleue, as described by Louis Arthur Etienne
Fallot in 1888 [1], is the clinical description of the physiology
created by a combination of anatomic malformations
now referred to as tetralogy of Fallot. The cardinal
features (Figure 1) consist of an interventricular communication,
or ventricular septal defect, biventricular connection
of the aortic root, which overrides the muscular
ventricular septum, obstruction of the right ventricular
outflow tract, and right ventricular hypertrophy [2]. Each
component can vary in its severity, with the variation
directly affecting the manifestation and management of
the disease.