(spontaneous type 1 ECG pattern, familial juvenile SD, and þEPS)
displayed limited clinical value, mainly owing to its low specificity
(21%–61%) and low positive predictive value (9%–15%).
CONCLUSIONS In patients with type 1 Brugada ECG pattern, most
arrhythmic events occur in patients with an ICD while SD is rare in
patients without an ICD. While we have an acceptable ability to
predict ICD-FVA, we have insufficient data to predict SD.
KEYWORDS Brugada syndrome; Ventricular arrhythmias; Risk
stratification; Sudden death; Implantable cardioverter-defibrillator
ABBREVIATIONS ECG ¼ electrocardiogram/electrocardiographic;
þEPS ¼ positive electrophysiologic study; EPS ¼ negative
electrophysiologic study; ICD ¼ implantable cardioverterdefibrillator;
ICD-FVA ¼ implantable cardioverter-defibrillator–
recorded fast ventricular arrhythmias; PPV ¼ positive predictive
value; NPV ¼ negative predictive value; SD ¼ sudden death
(Heart Rhythm 2014;11:252–258) I 2014 Heart Rhythm Society. All
rights reserved.