Results
All patients were followed up. Forty-two patients (20%) died, 36 women and 6 men, at a mean age of 62 years (women 61 ± SD 14, men 64 ± 19 years). More deaths were observed than expected (SMR = 2.4, 95% CI 1.7 to 3.0). CVM was the predominant cause of death (n = 20, 48%) (Table 1). At inclusion, 124 patients were between 40 and 65 years of age. In this group, we observed nine cardiovascular deaths within 10 years.