The major systemic treatments that were adopted in addition to
supportive care were corticosteroids, IVIG, and plasmapheresis. The
treatments performed are shown in Table 3. All cases, except 2
cases of SJS and 1 case of TEN, were treated with corticosteroids
with or without other therapies. Prompt tapering of the steroid
dose was performed along with amelioration of symptoms. In SJS,
most cases (45 cases, 86.5%) were treated with corticosteroids
alone. Of the cases, 18 (34.6% of all SJS) were performed pulse
therapy (500e1000 mg/day of methylprednisolone for 3 days). On
the other hand, in TEN, steroid pulse therapy was performed in 31
cases (88.6%) of all cases. Less than half cases (14 cases, 40%) were
treated with corticosteroids alone and among them 12 cases were
performed pulse therapy (500e1000 mg/day of methylprednisolone
for 3 days). The case treated without steroid was a 62-year-old
woman who was treated with IVIG (20 g/day for 2 days) alone,
because she had acquired Methicillin-resistance Staphylococcus
aureus (MRSA) pneumonia after the operation of acute aorta
dissection when she developed TEN. IVIG was highly effective in
this case and resulted in remarkable recovery from the TEN
eruption