β-Hexosaminidase activity was measured in plasma and leucocytes with the use of the synthetic substrate 4-methylumbelliferyl-2-acetamido-2-deoxy-β-D-gluco-pyranoside (MUG) and the % Hex A was determined using heat denaturation, as described previously
β-Hexosaminidase activity was measured in plasma and leucocytes with the use of the synthetic substrate 4-methylumbelliferyl-2-acetamido-2-deoxy-β-D-gluco-pyranoside (MUG) and the % Hex A was determined using heat denaturation, as described previously