Table 1. Updated Clinical Classification of Pulmonary Hypertension.
1. Pulmonary Arterial Hypertension
1.1 Idiopathic
1.2 Heritable
1.2.1 Bone morphogenic protein receptor, type 11
1.2.2 Activin receptor-like kinase 1, endoglin (with or without hereditary hemorrhagic telangiectasis)
1.2.3 Unknown
1.3 Drug- and toxin-induced
1.4 Associated with associated pulmonary arterial hypertension
1.4.1 Connective tissue disease
1.4.2 HIV infection
1.4.3 Portal hypertension
1.4.4 Congenital heart disease
1.4.5 Schistosomiasis
1.4.6 Chronic hemolytic anemia
1.5 Persistent pulmonary hypertension of the newborn
1’ Pulmonary veno-occlusive disease and/or pulmonary capillary hemangiomatomasis