Background: Supernumerary ovary (ie, ovarian ectopia having no anatomic connection with the normally placed ovaries) is a rare gynecologic
condition. To the best of our knowledge, only 1 pediatric case of supernumerary ovary has been reported to date in the English literature.
Case: A 4-year-old girl was assessed for foul-smelling vestibular discharge and was found to have a fistulous tract with opening near the
vaginal orifice. Fistuloscopy revealed hair in the lumen of the tract. Computed tomography scan showed a retroperitoneal mass in
continuation of the tract. Excision of the mass revealed a mature teratoma in a retroperitoneal supernumerary ovary.
Summary and Conclusion: Supernumerary ovary, a gynecologic rarity, is even more uncommon in children. Hence, a thorough clinicalradiological-pathological
correlation is mandatory to diagnose extragonadal ovarian tumors arising in supernumerary ovaries.
Key Words: Supernumerary, Ovary, Mature teratoma, Retroperitoneum, Pediatric